Paediatric ectopia lentis: clinical profile and evolution

Session Details

Session Title: Paediatric Ophthalmology & Other Topics

Session Date/Time: Tuesday 25/09/2018 | 08:00-10:30

Paper Time: 08:18

Venue: Room A3, Podium 2

First Author: : I.Hajji MOROCCO

Co Author(s): :    L. Soltani   H. Ahammou   A. Moutaouakil              

Abstract Details

Purpose:

Ectopic lentis is defined displacement of the natural crystalline lens. The most common etiologies for ectopia lentis are Marfan syndrome, simple ectopia lentis, ectopia lentis et pupillae, and homocystinuria. We present a case series of patients seen at our institution with ectopia lentis and report their surgical and visual outcomes .

Setting:

ophthalmological department, ARRAZI hospital, university hospital Mohamed VI medical school, caddi ayyad university

Methods:

A retrospective chart review was conducted of all pediatric ectopic lentis treated in our departement with lensectomy from January 2014 to October 2017.

Results:

We analyzed data from 29 consecutive patients with bilateral ectopic lenti. The mean age of the patients was 6 years. The most common etiologies were Marfan syndrome in 24 eyes. Preoperative best-corrected visual acuity was less than 20/200. Ocular examination showed non complicated subluxation of the lens in 54 cases. Other ocular abnormalities were found in 9 children, glaucoma was seen in 6 cases. All eyes underwent lensectomy and anterior vitrectomy. The visual rehabilitation was based on postoperative correction of aphakia with amblyopia treatment. Postoperative best-corrected visual acuity was > 20/40 at last follow-up in 35% of eyes.

Conclusions:

Management of ectopia lentis in the child can be challenging, particularly because of the risk for developing amblyopia. Anterior lensectomy and vitrectomy, aphakic correction followed by managment of amblyopia provide a consistent visual outcome in young patients with ectopia lentis.

Financial Disclosure:

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