Posters

Bilateral and symmetrical Peters anomaly type I presentation in newborn: case report

Poster Details

First Author: L. Coelho BRAZIL

Co Author(s):    G. Muinhos   H. Almeida   L. Barbosa   G. Vasconcelos           

Abstract Details

Purpose:

Peters anomaly type I is a rare congenital ocular disorder, characterized by a central corneal opacity with iridocorneal adhesions without cataract. We report a case of a newborn with bilateral and symmetrical Peters anomaly type I that underwent to bilateral corneal transplantation and bilateral glaucoma surgery, in the first five months of life, in order to get a good visual prognosis.

Setting:

IOBH (Eye Institute of Belo Horizonte), Minas Gerais, Brazil.

Methods:

Clinical case report of a boy two months old, referred due to bilateral corneal opacity and glaucoma since his birth. The baby responds to light in all tested fields. In the examination under narcosis, there was central corneal opacity, with clear corneal periphery and deep anterior chamber bilaterally. The corneal diameter was 11 mm in both eyes and the intraocular pressure was 28 mmHg on the right eye and 18 mmHg on the left eye. The ultrasound biomicroscopy showed thickened cornea, thickened and shortened iris and lens opacity suspicion bilaterally. The ultrasound of posterior segment was normal in both eyes.

Results:

The boy underwent to penetrating keratoplasty, trabeculotomy and iridectomy on the right eye with three months old and on the left eye with four months old. There was no cataract. The patient was promptly referred to a pediatric ophthalmologist to proper amblyopia management and kept clinical follow-up with good surgical recovery.

Conclusions:

Congenital corneal opacities may result from hereditary, developmental or infectious causes. They represent a range of disease from unilateral to bilateral cases, associated or not with systemic malformations or ocular malformations. Early correct diagnosis of the disease and promptly appropriate treatment may prevent deprivation amblyopia, ensuring an adequate multidisciplinary approach.

Financial Disclosure:

NONE