Posters

Bilateral cataract surgery in congenital aniridia

Poster Details

First Author: T. Valadão BRAZIL

Co Author(s):    N. Maes   R. Souza   N. Garcia   A. Alves   L. Motta        

Abstract Details

Purpose:

To describe a case of a male patient, 28 years of age with total right eye aniridia and partial left eye aniridia, horizontal nystagmus and glaucoma, treating with beta blockers eye drops, presenting congenital bilateral cataracts with decrease of visual acuity (AV OR 0,1; AV OS 0,05). Bilateral congenital aniridia is a rare disorder and is characterized by a partial or total absence of the iris associated with foveal hypoplasia which leads to a reduction of the visual acuity and nystagmus since an early age. Mutations or intragenic deletions of the PAX6 gene represent the major causes of aniridia.

Setting:

Federal Hospital of Bonsucesso, Rio de Janeiro, Brazil

Methods:

For the treatment of the patient, the phacoemulsification surgery in both eyes at different times was the choice. The capsulorhexis were made continuous and circular with local anesthesia and the IOL's implanted in the capsular bags.

Results:

The surgeries were successful, there were no complications during the surgical acts. The patient reported qualitative improvement of vision, there was an improvement in final visual acuity two months after the last surgery, OR 0.2 and OS 0.25. There has been no reduction of nystagmus and is expected to PAX 6 gene analysis

Conclusions:

The surgeries were beneficial to the patient, improving the quality of vision and the final visual acuity. Over time, the anterior capsule opacification create a diaphragm effect

Financial Disclosure:

NONE