Posters

Corneal dystrophy of Groenouw (type II): about 2 families

Poster Details

First Author: M.Elmhadi MOROCCO

Co Author(s): N. Elhalouat   A. Alami   J. Laayoun   A. Bouzidi   S. Iferkhass   A. Laktaoui     

Abstract Details

Purpose:

Groenouw II dystrophy is certainly a rare condition, with essentially a clinical diagnosis. The purpose of this work is to demonstrate through these 2 families the clinical characteristics of this pathology to facilitate its diagnosis.

Setting:

Ophthalmology service - Military Hospital Moulay Ismail of Meknès - Morocco.

Methods:

We report the case of 2 families each composed of 2 siblings, admitted to the ophthalmic consultation for a visual loss with corneal lesions of slowly progressive installation.

Results:

The first family : 42 year old man and 23 year old woman, from a consanguineous marriage. Ophthalmologic examination found a collapsed visual acuity and presence of gray and whitish central opacities, of small size ; that sit in the anterior stroma and diffuse in depth. The second family: Two men aged 32 and 29, from a consanguineous marriage. Ophthalmologic examination revealed a collapsed visual acuity and snowflakes whitish corneal deposits centered on the visual axis separated by healthy cornea zones and in section located of the anterior stroma.

Conclusions:

Groenouw II dystrophy, is a hereditary dystrophy transmitted in an autosomal recessive manner, clinically distinguished by gray and whitish opacities of small diameters, with distinct contours classically arranged in the anterior stroma. When visual acuity is too affected, apart from the symptomatic treatment and physical or chemical abrasions of the superficial cornea, therapeutic excimer laser photokeratectomy has become essential. The forms causing blindness require lamellar or transfixing keratoplasty with a risk of recurrence in the graft. Due to the hereditary nature of the pathology, an extensive search for similar cases in the patient's family is required.

Financial Disclosure:

None