Posters
Limbal dermoid mass: a case report
Poster Details
First Author: F.Caiado PORTUGAL
Co Author(s): S. Mano W. Rodrigues
Abstract Details
Purpose:
To report a challenging case of Limbal Dermoid (LD) with multimodal imaging evaluation. It��s a congenital benign tumor of normal tissue of ectodermal or mesodermal origin in an abnormal location, and evaluate difficulties in diagnosis, progression and treatment options.
Setting:
Ophthalmology Department, Hospital de Santa Maria, University of Lisbon
Methods:
Observational case report of a six-year-old child presenting a temporal-superior gelatinous keratoconjunctival lesion in the right eye with feeder vessels, stromal involvement and rapid centric-corneal progression who underwent comprehensive ophthalmic examination, incisional biopsy and multimodal imaging with ultrassound biomicroscopy (UBM) and orbit computerized tomography (CT) scan.
Results:
During evaluation, two consecutive biopsies excluded neoplastic tissue, UBM excluded scleral and uveal involvement and spontaneous regression of its limbic component despite continuous growth towards visual axis was observed. Given the age of presentation, partial regression and exclusion of neoplastic tissue the clinical diagnosis of limbal dermoid was made. CT scan revealed no orbital involvement and systemic examination excluded associated syndromes. Due to progressive decreased BCVA (20/25 to 20/100) and risk of amblyopia penetrating keratoplasty was performed. At 12-month follow-up BCVA improved to 20/32 and there was no sign of recurrence.
Conclusions:
Limbal neoformations have a variable presentation in children and is mandatory to exclude malignant lesions and systemic conditions. Limbal dermoids showing progressive growth or affecting the pupillary area have indication for surgical treatment, whose options are limited in the presence of full-thickness corneal involvement.
Financial Disclosure:
NONE
