Posters

Alveolar soft part sarcoma: an uncommon presentation in adult

Poster Details

First Author: N.Kosaiyaganonth THAILAND

Co Author(s):    R. Khotcharrat                    

Abstract Details

Purpose:

An alveolar soft part sarcoma (ASPS) is a rare soft tissue tumor, representing 0.2-0.9% of all soft tissue sarcomas. The tumor is characterized by a painless, soft and slow-growing mass during the adolescent until adulthood. In adult patients, it usually affects extremities, but in young patients, head and neck lesion is more common. Despite ASPS is a slow-growing tumor, metastasis often occurs. Surveillance has an important role in these patients. We would like to present the case of a 23-year-old woman with an uncommon presentation of ASPS.

Setting:

A Thai 23-year-old woman with progressive left eye proptosis was referred to Naresuan University Hospital, the tertiary care setting.

Methods:

We reviewed the medical records of the patient from September 2007 to July 2015. Prior case reports and case series were revised. The information was collected and the computerized tomography and the tissue pathology were reviewed and discussed.

Results:

A Thai 23 years old female presented with progressive proptosis of the left eye for 4 months. The visual acuity was 20/20 at the first visit with normal visual fields and RAPD positive on the left. Her extraocular muscle movement of the left eye was limited by 20%. Ultrasonography of left orbit found high vascular soft tissue mass with pressure effect on the globe and optic nerve deviation. The computerized tomography presented left orbital mass with anterolateral inferior orbital displacement. Her thyroid function test was within normal limits. The neurosurgeon was consulted for tumor removal. The tissue diagnosis was ASPS.

Conclusions:

Even the ocular presentation of ASPS is rare in adults, but it happens. If we early detect the tumor and can resect all the primary tumor, we may increase the survival rate of the patients. This is a case report of adult ASPS with ocular presentation who treated with surgery alone and has no recurrence after 8 years from the resection.

Financial Disclosure:

None